Adipositas cordis: a challenging differential diagnosis

Authors

  • Cristiane Rúbia Ferreira Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
  • Fernando Peixoto Ferraz de Campos Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
  • Jorge Isaac Garcia Paez Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP - Brasil.

DOI:

https://doi.org/10.4322/acr.2016.013

Keywords:

Adipose tissue/pathology, Cardiomiopathy, Restrictive Cardiomiopathy, Arrhythmogenic right ventricle displasia, Hypotension, Death.

Abstract

Myocardial fatty infiltration is a diagnostic challenge for clinicians and pathologists once it may be found as part of normal myocardial tissue or may be a manifestation of diseases responsible for fatal outcomes like sudden death, arrhythmias and heart failure.
Differential diagnosis between the diseases related to myocardial fatty infiltration as, Adipositas Cordis and Arrhythmogenic Dysplasia of the Right Ventricle requires
clinical, laboratory and histopathological correlation.
The authors present a case of a previously healthy patient, non obese, who unexpectedly presented a refractory hypotension after a physiologic stress characterized by immediate post operatory.
The necropsy findings showed fatty infiltration of the heart characterizing the histological features of Adipostas Cordis. This finding explained the right ventricle failure and consequent refractory hypotension.

Downloads

Download data is not yet available.

Author Biographies

  • Cristiane Rúbia Ferreira, Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
    Serviço de Anatomia Patológica do Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
  • Fernando Peixoto Ferraz de Campos, Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
    Divisão de Clínica Médica do Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brasil.
  • Jorge Isaac Garcia Paez, Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP - Brasil.
    Departamento de Moléstias Infecciosas e Parasitárias da Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP - Brasil.

Published

2011-03-08

Issue

Section

Article / Autopsy Case Report

How to Cite

Ferreira, C. R., de Campos, F. P. F., & Paez, J. I. G. (2011). Adipositas cordis: a challenging differential diagnosis. Autopsy and Case Reports, 1(1). https://doi.org/10.4322/acr.2016.013